What is Heterotaxy Syndrome?
Heterotrophy syndrome is an abnormal condition that occurs in the heart and organs in other bodies. If the normal human stomach is on the right, the Baby's stomach is on the left.
Rare syndrome is arguably no cure, the patient must often undergo surgery along with the development of the body but fortunately this syndrome is only owned by some babies from many couples around the world.
The potential life of this syndrome sufferers is very minimal because abnormal gastric position can affect the stomach and the heart that is nearby
And this is the result of research analyzed through openheart.bmj.com
There were 35 patients diagnosed with heterotaxy syndrome, 17 of whom were diagnosed antenatally. 22 patients had right atrial isomerism and 13 had left atrial isomerism. The median age of postnatal diagnosis was 2.5 days old (1 day to 19 months). 12 patients had a poor outcome; 6 patients died, 1 underwent cardiac transplantation and 5 had an NYHA functional class of >III. 5 patients had a biventricular repair and the remaining 30 had a univentricular repair. Type of atrial isomerism, univentricular or biventricular anatomy, severity of atrioventricular valve regurgitation or ventricular dysfunction, obstructed pulmonary venous return, occurrence of arrhythmia and presence of pulmonary atresia did not predict poor outcome. Fetal diagnosis also did not confer a survival advantage. The median duration of follow-up in this cohort was 65 months (2 days to 16.8 years).
Conclusions Survival for patients with heterotaxy syndrome was 83% over a median follow-up of 65 months. 34% of patients had a poor outcome. None of the variables studied were predictive of death, transplantation or NYHA classification III or IV.
And these are the kinds of possibilities that will occur for the heterotaxty sufferer
- Immune glands that are not perfect resulting in decreased immunity and more susceptible to infection, especially at the age of the baby
Digestive disorders resulting from abnormal bile secretion systems and structures and bowel positions that are incompatible with the digestive tract
-Distence of blood vessel function
-Infection of the lung due to cilia or hair on the inside of the lung can not filter air and germs that enter the respiratory tract
-Disruptive pulmonary function that causes difficulty breathing and channel oxygen throughout the body that can cause growth disorders
- Impaired liver function characterized by symptoms jaundice, skin discoloration and eye condition to yellow.
Consumption of antibiotics for patients is necessary, but it must pass a diagnosis from the doctor, and the only thing that needs to be done the patient is to keep the heart and stomach remain healthy without any disturbance, including ulcers that attack the stomach
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